HADHA Rabbit pAb - diagbio | 戴格生物

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HADHA Rabbit pAb

db7073

Product Name : HADHA Rabbit pAb

Cat.No.: db7073

Synonyms : GBP; ECHA; HADH; LCEH; MTPA; LCHAD; TP-ALPHA

Application : WB, ICC/IF, FC, IP

Reactivity : Human, Mouse, Rat

Host species : Rabbit

Background This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008]
Immunogen A synthetic peptide of human HADHA
Gene ID 3030
Swiss Prot P40939
Synonyms GBP; ECHA; HADH; LCEH; MTPA; LCHAD; TP-ALPHA
Reactivity Human, Mouse, Rat
Application WB, ICC/IF, FC, IP
Recommended dilution WB: 1:1000
ICC/IF: 1:50
FC: 1:20
IP: 1:20
Calculated MW 83 kDa
Observed MW 78 kDa
Host species Rabbit
Clonality Polyclonal
Isotype IgG
Purity Affinity Purification
Conjugation Un-conjugated
Storage/Stability Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.

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