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SGSH (DGR15419) Rabbit mAb
Alternate Text
db15060
Datasheet

Product Name : SGSH (DGR15419) Rabbit mAb

Cat.No.: db15060

Synonyms : HSS; SFMD; MPS3A

Application : WB, ICC/IF

Reactivity : Human

Host species : Rabbit

  • Background This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
  • Immunogen Recombinant protein of human SGSH
  • Gene ID 6448
  • Swiss Prot P51688
  • Synonyms HSS; SFMD; MPS3A
  • Reactivity Human
  • Application WB, ICC/IF
  • Recommended dilution WB: 1:1000
    ICC/IF: 1:100-1:200
  • Calculated MW 57 kDa
  • Observed MW 57 kDa
  • Host species Rabbit
  • Clonality Monoclonal
  • Clonality No. DGR15419
  • Isotype IgG
  • Purity Affinity Purification
  • Conjugation Un-conjugated
  • Storage/Stability Store at -20°C. Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
  • Western blot analysis of extracts from MCF-7 cells using db15060 at 1:1000.
  • Western blot analysis of extracts from HepG2 cells using db15060 at 1:1000.
订购信息
  • Package Price (RMB)
  • 10μL 398
  • 20μL 698
  • 50μL 1398
  • 100μL 2398
  • 货期:现货
For research use only. Not intended for diagnostic.