SGSH (DGR15419) Rabbit mAb
Product Name :
SGSH (DGR15419) Rabbit mAb
Cat.No.:
db15060
Synonyms :
HSS; SFMD; MPS3A
Application :
WB, ICC/IF
Reactivity :
Human
Host species :
Rabbit
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Background
This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
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Immunogen
Recombinant protein of human SGSH
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Gene ID
6448
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Swiss Prot
P51688
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Synonyms
HSS; SFMD; MPS3A
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Reactivity
Human
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Application
WB, ICC/IF
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Recommended dilution
WB: 1:1000
ICC/IF: 1:100-1:200
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Calculated MW
57 kDa
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Observed MW
57 kDa
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Host species
Rabbit
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Clonality
Monoclonal
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Clonality No.
DGR15419
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Isotype
IgG
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Purity
Affinity Purification
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Conjugation
Un-conjugated
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Storage/Stability
Store at -20°C. Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
×
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Western blot analysis of extracts from MCF-7 cells using db15060 at 1:1000.
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Western blot analysis of extracts from HepG2 cells using db15060 at 1:1000.
订购信息
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Package
Price (RMB)
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10μL
398
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20μL
698
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50μL
1398
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100μL
2398
- 货期:现货
For research use only. Not intended for diagnostic.