GAA (DGR18865) Rabbit mAb (PBS Only)
Product Name :
GAA (DGR18865) Rabbit mAb (PBS Only)
Cat.No.:
db14623-PBS
Synonyms :
LYAG
Reactivity :
Human, Mouse, Rat
Host species :
Rabbit
Conjugation/Formulation:PBS Only
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Background
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]
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Immunogen
A synthetic peptide of human GAA
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Gene ID
2548
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Swiss Prot
P10253
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Synonyms
LYAG
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Reactivity
Human,Mouse,Rat
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Application
WB
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Recommended dilution
WB: 1:1000-1:5000
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Calculated MW
105 kDa
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Observed MW
76 kDa
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Host species
Rabbit
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Clonality
Monoclonal
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Clonality No.
DGR18865
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Isotype
IgG
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Purity
Affinity Purification
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Conjugation
Un-conjugated
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Concentration
1 mg/ml
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Formulation
PBS Only
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Storage/Stability
Store at -20°C. Recommended to aliquot into single-use vials. Supplied in 1X PBS (pH 7.4). BSA and Azide Free. Stable for 12 months from date of receipt.
×
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Western blot analysis of extracts from 293T cells and Human placenta tissue using
db14623
订购信息
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Package
Price (RMB)
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100μg
4498
- 货期:现货
For research use only. Not intended for diagnostic.