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GAA (DGR18865) Rabbit mAb (PBS Only)
db14623-PBS
Datasheet

Product Name : GAA (DGR18865) Rabbit mAb (PBS Only)

Cat.No.: db14623-PBS

Synonyms : LYAG

Application:

Reactivity : Human, Mouse, Rat

Host species : Rabbit

Conjugation/Formulation:PBS Only

  • Background This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]
  • Immunogen A synthetic peptide of human GAA
  • Gene ID 2548
  • Swiss Prot P10253
  • Synonyms LYAG
  • Reactivity Human,Mouse,Rat
  • Application WB
  • Recommended dilution WB: 1:1000-1:5000
  • Calculated MW 105 kDa
  • Observed MW 76 kDa
  • Host species Rabbit
  • Clonality Monoclonal
  • Clonality No. DGR18865
  • Isotype IgG
  • Purity Affinity Purification
  • Conjugation Un-conjugated
  • Concentration 1 mg/ml
  • Formulation PBS Only
  • Storage/Stability Store at -20°C. Recommended to aliquot into single-use vials. Supplied in 1X PBS (pH 7.4). BSA and Azide Free. Stable for 12 months from date of receipt.
  • Western blot analysis of extracts from 293T cells and Human placenta tissue using db14623
订购信息
  • Package Price (RMB)
  • 100μg 4498
  • 货期:现货
For research use only. Not intended for diagnostic.