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Product Name : GAA (DGR18865) Rabbit mAb
Cat.No.: db14623
Synonyms : LYAG
Application：
Reactivity : Human, Mouse, Rat
Host species : Rabbit
Conjugation/Formulation：Un-conjugated
- Background This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]
- Immunogen A synthetic peptide of human GAA
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Gene ID
2548
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Swiss Prot
P10253
- Synonyms LYAG
- Reactivity Human,Mouse,Rat
- Application WB
- Recommended dilution WB: 1:1000-1:5000
- Calculated MW 105 kDa
- Observed MW 76 kDa
- Host species Rabbit
- Clonality Monoclonal
- Clonality No. DGR18865
- Isotype IgG
- Purity Affinity Purification
- Conjugation Un-conjugated
- Storage/Stability Store at -20°C. Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
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Western blot analysis of extracts from 293T cells and Human placenta tissue using db14623 at 1:1000.
订购信息
- Package Price (RMB)
- 10μL 398
- 20μL 698
- 50μL 1398
- 100μL 2398
- 货期：现货
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For research use only. Not intended for diagnostic.
